Carnitine Biosynthesis Pathway

The video tutorial explains the importance of carnitine as a metabolite that transports long-chain fatty acids into the mitochondria. It covers how carnitine is synthesized in the body from lysine and methionine, with a focus on the biosynthesis pathway involving several enzymes. The tutorial details the enzymatic reactions and cofactors required for carnitine synthesis, highlighting the role of the kidney and the conservation of the pathway across species. The final steps of the synthesis process are discussed, along with carnitine's role in beta-oxidation.

Explain the role of vitamin C in the carnitine biosynthesis pathway.

Describe the process of how 4-trimethylaminobutyric aldehyde is converted to L-carnitine.

What is the significance of L-carnitine in fatty acid metabolism?