Glycogen, Glycolysis, Gluconeogenesis, and Sugars

Which disease states are associated with FASTING hypoglycemia?

• Type 0

• Cori Disease

• MODY

• Hers

• Von Gierke

Which of the following disease states is NOT associated with hypoglycemia?

• Type 0

• MODY

• Hers

• Von Gierke

• Cori

Which of the following is associated with decreased glycogen storage AND muscle weakness?

• MODY

• Type 0

• McArdle

• Tauri

Which of the following are associated with enlarged liver?

• Anderson

• Cori

• Von Gierke

• MODY

• Hers

Match the disease with the reason it causes enlarged liver:

• Inability to break down glycogen

• Hers

• Does not cause enlarged liver

• Type 0

• Inability to release glycose

• Anderson

• Inability to branch glycogen

• Von Gierke

• Inability to remove branches on glycogen

• Cori

Which of the following is diet one of the branches of treatment?

• Cori

• Hers

• Von Gierke

• McArdle

• Anderson

Which of the following diseases is associated with hyperglycemia?

• MODY

• McArdle

• Tauri

• Type 0

• Cori

Which of the following diseases is associated with muscle weakness?

• Tauri

• McArdle

• Cori

• Anderson

• Von Gierke

What disease is a defect in the first step of glycolysis?

• MODY

• Anderson

• Type 0

• Von Gierkes

Match the GLUT with the associated cells:

• Neurons

• GLUT 4

• Lumen side of intestine

• GLUT 3

• Intestine, β cells, Liver

• GLUT 1

• Muscle and Fat

• GLUT 5

• RBC, BBB

• GLUT 2