Thalassemia care

What is the type of thalassemia inheritance?

• Autosomal dominant

• Autosomal recessive

• X-linked dominant

• X-linked recessive

Which of the following is a characteristic of severe thalassemia?

• Hb < 8 g/dL

• first blood transfusion within 5 years old

• Anemia with anemic symptom within 2 years

• Preserve growth

Which one is not a goal for screening Thalassemia?

• Homozygous B-thalassemia

• B-thalassemia/HbE

• Homozygous HbE disease

• Hb Bart’s hydrops fetalis

Which one is false about blood transfusion in TDT?

• LDPRC type

• Fresh donate blood (<7days)

• 10-15 cc/kg/dose

• Keep pre transfusion Hb 7-9 g/dL

Which of the following is the indication of iron chelation in TDT?

• Serum ferritin > 1000 ng/mL

• LIC > 5 mg/g dry weight of liver

• Regularly transfused > 5 times

• MRI cardiac T2 >20 msec

Which one is true about monitoring complication in thalassemia patient?

• Monitor growth velocity every year

• Screen puberty at 14 years old in girls

• Screening blood glucose at age >9 years in NTDT

• Screening Anti-HIV every year in TDT patients

Which one is the post splenectomy vaccination?

• Pneumococcal vaccine

• Hib vaccine

• Meningococcal vaccine

• All

What is the main goal of managing thalassemia?

• Minimizing the need for transfusions
• Reducing the amount of iron in the body
• Improving overall quality of life
• Increasing the body's immunity